Flashcards on Congenital Hand Contractures in Pediatrics

Congenital Hand Contractures in Pediatrics: Comprehensive Guide

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What is camptodactyly?

A painless flexion contracture of the proximal interphalangeal (PIP) joint that is usually gradually progressive and occurs without intra-articular or

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Pediatric Camptodactyly

80 cards

Card 1

Question: What is camptodactyly?

Answer: A painless flexion contracture of the proximal interphalangeal (PIP) joint that is usually gradually progressive and occurs without intra-articular or

Card 2

Question: Which joints are typically not affected by camptodactyly?

Answer: The metacarpophalangeal (MP) and distal interphalangeal (DIP) joints; though compensatory deformities may develop.

Card 3

Question: How is camptodactyly classified in terms of reducibility?

Answer: It is divided into a flexible (reducible) form and a fixed (irreducible) form, with different treatment algorithms for each.

Card 4

Question: What is known about the etiology and pathogenesis of camptodactyly?

Answer: The precise etiology is unknown with no consensus; almost every structure around the PIP joint has been implicated, including skin/subcutaneous tissue

Card 5

Question: Name some proposed skin and subcutaneous tissue changes implicated in camptodactyly.

Answer: Dermal deficiency or contracture and fibrotic changes within subcutaneous tissue or fascia.

Card 6

Question: What periarticular alterations have been proposed as contributors to camptodactyly?

Answer: Contractures of the collateral ligaments or volar plate (or both).

Card 7

Question: Which musculotendinous structures have been implicated in camptodactyly?

Answer: Abnormalities of the flexor tendons, intrinsic muscles (lumbricals and interossei), and the extensor apparatus.

Card 8

Question: How common is camptodactyly in the general population?

Answer: It occurs in less than 1% of the population.

Card 9

Question: Are most cases of camptodactyly symptomatic or asymptomatic?

Answer: Most cases are mild and asymptomatic and probably do not warrant evaluation.

Card 10

Question: Is camptodactyly usually sporadic or inherited?

Answer: Most cases are sporadic, but it can be inherited as an autosomal dominant trait with variable expressivity and incomplete penetrance.